NON-COMPACTED CARDIOMYOPATHY: A CASE OF SEVERE HEART FAILURE

Abstract

Non-compacted cardiomyopathy is a rare congenital anomaly, characterized by alteration of the cardiac structure, with the formation of a thin and compacted epicardial layer and an extensive trabeculated, uncompacted endocardial layer, with deep recesses that can lead to Heart Failure, thromboembolic phenomena and arrhythmias. In this article we present the case of a 59-year-old woman, a heavy smoker, who, because of complaints of fatigue to ordinary physical activity and the appearance of a complete left bundle branch block, was submitted to an echocardiography that revealed a severe systolic dysfunction due to global hypokinesia. Subsequently, a coronary catheterization was performed that did not show any alterations, so a cardiac magnetic resonance was requested, which revealed dilated cardiomyopathy, as well as myocardial trabeculation, mainly in the middle and apical, anterior, lateral and inferior segments, confirming the diagnosis. Despite always being in the NYHA II stage, due to a severe decrease in the ejection fraction, a CRT-D was placed. This case demonstrates a rare cause of Heart Failure that needs to be diagnosed as early as possible, in order to avoid its possible complications.